Methaemoglobinaemia

physiology

MetHb = Hb containing Fe3+
Suggests exposure to oxidative stress
homeostasis usually via reductive mecahnisms including cytochrome b5 reductase

Headline
Etiology ➥ Clinical state - anything to cause prolonged oxidative stress? e.g. sepsisssss
➥ Toxins: nitrites (e.g. amyl nitrite/poppers); local anaesthetics, methylene blue (!! in high doses...), metoclopramide, aniline dyes...
➥ PMH: Inborn errors of metabolism
Clinical presentation Non-specific, but mainly hypoxic symptoms.
Cyanosis, 'happy hypoxia'
Diagnostic investigations ABG, or specifically request from lab
- Use to calculate saturation gap = SaO2 - SpO2
- >5% implies abnormal hb
Differentials
Immediate management A/B: FiO2 100% (maximise functional Hb)
IV glucose? (physiologically sound. maybe, maybe not.)
Methylene blue (...hmm)
Consider exchange transfusion
Toxbase it, as always
Ongoing management