SJS TEN

it's like a burn, but not quite
< 10% BSA = SJS
10-30% BSA = SJS/ TEN overlap syndrome
> 30%= TEN
Etiology Drugs: phenytoin, penicillins, quinolones, NSAIDs
Non-drugs: Mycoplasma pneumonia, HIV, HSV, Mumps...
Epidemiology
Clinical presentation - mucocutaneous lesions: papules/vesicles → clusters, nonpruritic involving all mucous membranes (oropharynx, airway, urethra, cornea) -> rupture leaving denuded skin
- looks like an extreme sunburn
Pathogenesis
Diagnostic investigations Clinical diagnosis
Ddx: staph scalded skin syndrome/toxic shock syndrome
Management Like a severe burn:
A: may require sedation → intubation
B: may have tracheal involvement?!
C: hypovolaemic, hyperdynamic circulation. will require long lines, care with dressings
D: analgesia++ requirements
E: hypophosphataemia due to tissue regrowth; free water losses++
F: not as much as burns, really
G: high protein and calorie requirements
H: VTE risk complicated by lack of skin to place TEDS and IPCs
I: abx-coated lines, no steroids

SCORTEN = prognostic criteria

Age > 40 years
Presence of a malignancy
Heart rate > 120
Initial percentage of epidermal detachment > 10%
Serum urea level > 10 mmol/L
Serum glucose level > 14 mmol/L
Serum bicarbonate level < 20 mmol/L.