ejection systolic murmur

pulmonary stenosis

Headline
Etiology carcinoid heart syndrome, rheumatic fever.
Congenital syndromes: tetralogy of Fallot, Noonan syndrome, rubella, Turner's syndrome
Epidemiology
Clinical presentation - heave, JVP: large a wave; ejection systolic murmur
- Right heart failure
Pathogenesis
Diagnostic investigations ECG: R axis deviation, p-pulmonale, RBBB, RVH
Management Cardiac catheterisation is diagnostic
Mx: Valvuloplasty or valvotomy
Prevention