cardiomyopathies

see HOCM

Dilated
Etiology Associations: alcohol, hypertension, HH, pregnancy, thyrotoxicosis, chemotherapy (dauno/doxorubicin), Muscular dystrophy.
Epidemiology
Clinical presentation ↑ HR, ↓ BP, S3 gallop, MR/TR/ pleural effusion, oedema, jaundice, hepatomegaly, ascites
Pathogenesis nuclear hypertrophy, interstitial fibrosis, lymphocytic infiltration
Diagnostic investigations
Management Manage the heart failure
Constrictive
Etiology idiopathic, rheum (amyloid, sarcoid, scleroderma), haemochromatosis.
Epidemiology
Clinical presentation Similar to constrictive pericarditis
Pathogenesis "rubbery, non-compliant” myocardium, bilat hypertrophy; eosinophilic deposition/honeycomb pattern around myocytes
Diagnostic investigations Echo - diastolic dysfunction
Management Manage the heart failure
Complications: Pulmonary hypertension, SOB, R ventricle hypertrophy